A case of Dyke-Davidoff-Masson syndrome in Korea / 소아과
Korean Journal of Pediatrics
;
: 208-211, 2006.
Article
in English
| WPRIM
| ID: wpr-229107
ABSTRACT
Dyke-Davidoff-Masson Syndrome (DDMS) is a rare condition characterized by asymmetry of cerebral hemispheric growth with atrophy on one side, ipsilateral compensatory osseous hypertrophy, and contralateral hemiparesis. We experienced a 17 month-old male who presented with left focal clonic or tonic-clonic seizures accompanied by left hemiparesis and developmental delay. Brain MRIs demonstrated progressive atrophy of the right cerebral hemisphere with dilatation of the lateral ventricle, expansion of the ipsilateral frontal sinus with calvarial thickening, and elevation of the petrous pyramid and orbital roof. Brain SPECT showed a decreased volume of the right hemisphere with reduced blood flow. We therefore report a case of DDMS with a review of the literature.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Orbit
/
Paresis
/
Petrous Bone
/
Atrophy
/
Seizures
/
Brain
/
Magnetic Resonance Imaging
/
Tomography, Emission-Computed, Single-Photon
/
Lateral Ventricles
/
Dilatation
Limits:
Humans
/
Infant
/
Male
Country/Region as subject:
Asia
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2006
Type:
Article
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