Clinical analysis of lymphangioleiomyomatosis / 中国医学科学院学报
Acta Academiae Medicinae Sinicae
;
(6): 306-309, 2004.
Article
in Chinese
| WPRIM
| ID: wpr-231939
ABSTRACT
<p><b>OBJECTIVE</b>To improve the diagnosis and treatment of lymphangioleiomyomatosis (LAM).</p><p><b>METHODS</b>The clinical data of four cases of lymphangioleiomyomatosis diagnosed in our hospital were analyzed and corresponding literature was reviewed.</p><p><b>RESULTS</b>Lymphangioleiomyomatosis, a rare disorder of unknown cause that occured almost exclusively in women of child bearing ages, was characterized microscopically by atypical smooth muscle proliferation. It could occur as a sporadic diseases or as a part of tuberous sclerosis complex (TSC). LAM was associated with progressive dyspnea, recurrent spontaneous pneumothoraces, chylous effusions, and hamartomas.</p><p><b>CONCLUSION</b>Clinicians should be familiar with the characteristics of LAM so that diagnosis and treatment can be made earlier to improve the prognosis.</p>
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pathology
/
Biopsy, Needle
/
Diagnostic Imaging
/
Tomography, X-Ray Computed
/
Lymphangioleiomyomatosis
/
Diagnosis
/
Lung
/
Lung Neoplasms
Type of study:
Diagnostic study
Limits:
Adolescent
/
Adult
/
Female
/
Humans
/
Male
Language:
Chinese
Journal:
Acta Academiae Medicinae Sinicae
Year:
2004
Type:
Article
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