Absence of a Sphenoid Wing in Neurofibromatosis Type 1 Disease: Imaging with Multidetector Computed Tomography
Korean Journal of Radiology
;
: 70-72, 2006.
Article
in English
| WPRIM
| ID: wpr-24426
ABSTRACT
Neurofibromatosis type 1 disease is characterized by pigmented cutaneous lesions and generalized tumors of a neural crest origin and it may affect all the systems of the human body. Sphenoid dysplasia is one of the characteristics of this syndrome and it occurs in 5-10% of the cases; further, abnormalities of the sphenoid wings are often considered pathognomonic. However, complete agenesis of a sphenoid wing is very rare. We report here on an unusual case of neurofibromatosis type 1 disease with the associated absence of a sphenoid wing that was diagnosed by using multidetector computed tomography.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Sphenoid Bone
/
Tomography, X-Ray Computed
/
Neurofibromatosis 1
/
Imaging, Three-Dimensional
Limits:
Adult
/
Humans
/
Male
Language:
English
Journal:
Korean Journal of Radiology
Year:
2006
Type:
Article
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