A Case of Congenital Intrahepatic Portosystemic Shunt Associated with VSD Detected by Antenatal Sonography and Treated with Four Coil Embolizations and Open Heart Surgery after Birth
Journal of the Korean Society of Neonatology
;
: 176-182, 2008.
Article
in Korean
| WPRIM
| ID: wpr-28943
ABSTRACT
A congenital portosystemic shunt is a very rare portosystemic vascular anomaly which leads to jaundice, hypoglycemia, hyperammonemia, liver cirrhosis, hepatic coma, and pulmonary hypertension. Anatomically, portosystemic shunts are divided into intra- and extra- hepatic shunts. Congenital intrahepatic portosystemic shunts are rare anomalies, and the early diagnosis is important to prevent hepatic encephalopathy and hypoglycemia. We report a case of an infant with symptoms of heart failure due to a congenital intrahepatic portosystemic shunt and a ventricular septal defect (VSD), which were treated successfully with four coil embolizations and open heart surgery for the VSD.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Thoracic Surgery
/
Portasystemic Shunt, Surgical
/
Hepatic Encephalopathy
/
Hyperammonemia
/
Parturition
/
Early Diagnosis
/
Heart
/
Heart Failure
/
Heart Septal Defects, Ventricular
/
Hypertension, Pulmonary
Type of study:
Diagnostic study
/
Screening study
Limits:
Humans
/
Infant
Language:
Korean
Journal:
Journal of the Korean Society of Neonatology
Year:
2008
Type:
Article
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