Multifocal kaposiform hemangioendothelioma of soft tissue with bilateral pulmonary involvement in an adolescent / 소아과
Korean Journal of Pediatrics
;
: 500-504, 2014.
Article
in English
| WPRIM
| ID: wpr-29003
ABSTRACT
Kaposiform hemangioendothelioma (KHE) is a rare, locally aggressive vascular tumor of intermediate malignancy with resemblance to Kaposi sarcoma. It occurs predominantly in pediatric age groups as a cutaneous lesion with focal infiltration into the adjacent soft tissue and bone. Although visceral involvement is very uncommon, several cases with bone, retroperitoneal, or mediastinal involvement have been described. KHE has been reported to occasionally occur in unusual sites such as the thymus, tonsils, larynx, paranasal sinuses, deltoid muscle, spleen, uterine cervix, thoracic spine, and even the breast. Multifocal KHE is an extremely rare entity with few reports available in the literature, none of which describes pulmonary involvement. Herein, we report a unique case of multifocal KHE in a 13-year-old boy presenting with a huge soft tissue mass in the upper extremity complicated by bilateral pulmonary nodules that developed into large, necrotic tumor masses.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Paranasal Sinuses
/
Sarcoma, Kaposi
/
Spine
/
Spleen
/
Thymus Gland
/
Palatine Tonsil
/
Breast
/
Cervix Uteri
/
Upper Extremity
/
Deltoid Muscle
Limits:
Adolescent
/
Female
/
Humans
/
Male
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2014
Type:
Article
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