Your browser doesn't support javascript.
loading
Churg-Strauss syndrome in children: a case evolving in endomyocardiopathy / 中国当代儿科杂志
Article in Chinese | WPRIM | ID: wpr-317375
Responsible library: WPRO
ABSTRACT
A 13-year-old girl presented with a 1-month history of progressive exertional dyspnea (NYHA class IV) and exophthalmos for 6 months. She had a history of long-standing asthma and the presence of allergy. Hypereosinophilia and increased serum IgE levels (2472 IU/mL) were observed. Chest radiography and a high resolution CT scan documented a massive interstitial pulmonary infiltration. Echocardiography confirmed mild tricuspid regurgitation, apical obliteration of the right ventricle by fibrocalcific thickening of the endocardium and echogenic material suggestive of thrombosis. Churg-Strauss syndrome with cardiac involvement (endomyocardiopathy) was diagnosed. The patient received anticoagulation and corticosteroid therapy. In view of rapidly progressive severe endomyocardiopathy and stable hematology, the patient was referred for cardiac surgery. Histopathological examination of resected specimens confirmed laminated thrombus but without any trace of eosinophils embedded.
Subject(s)
Full text: Available Index: WPRIM (Western Pacific) Main subject: Pathology / Female / Humans / Churg-Strauss Syndrome / Adolescent / Endocardium / Endomyocardial Fibrosis Type of study: Case report Language: Chinese Journal: Chinese Journal of Contemporary Pediatrics Year: 2008 Type: Article

Similar

MEDLINE

...
LILACS

LIS

Full text: Available Index: WPRIM (Western Pacific) Main subject: Pathology / Female / Humans / Churg-Strauss Syndrome / Adolescent / Endocardium / Endomyocardial Fibrosis Type of study: Case report Language: Chinese Journal: Chinese Journal of Contemporary Pediatrics Year: 2008 Type: Article