Cutaneous Angiomyolipoma

ABSTRACT

Angiomyolipoma is a benign tumor, almost exclusively of the kidney, that is often associated with tuberous sclerosis. Cutaneous location is extremely rare. We report a case of cutaneous angiomyolipoma which occurred on the retroauricular area. A 57-year-old man presented with an asymptomatic mass on the retroauricular area. Although the clinical similarity to an epidermal or pilar cyst was striking, the histopathologic picture was distinctive. The tumor was a well-circumscribed subcutaneous mass composed of a mixture of smooth muscle, vascular spaces, and mature fat covered by a thin fibrous membrane.