A Case of Congenital Lymphatic Dysplasia Complicated by Hydrops Fetalis
Neonatal Medicine
; : 40-44, 2017.
Article
in Ko
| WPRIM
| ID: wpr-32565
Responsible library:
WPRO
ABSTRACT
Congenital lymphatic dysplasia is a rare congenital maldevelopment of the lymphatic system, in which dysfunction of the lymphatic system may cause leakage of lymph fluid into the limbs and the pleural, pericardial, or peritoneal cavity. We experienced a case of hydrops fetalis with subcutaneous lymphedema, chylothorax, chylous ascites and pericardial effusion. Lymphangiography revealed a critical defect of lymphatic system. Here, we report the first case of premature infant with congenital lymphatic dysplasia confirmed by lymphangiography, which is the first reported in Korea.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Pericardial Effusion
/
Peritoneal Cavity
/
Infant, Premature
/
Lymphography
/
Hydrops Fetalis
/
Chylous Ascites
/
Chylothorax
/
Edema
/
Extremities
/
Korea
Limits:
Humans
/
Newborn
Country/Region as subject:
Asia
Language:
Ko
Journal:
Neonatal Medicine
Year:
2017
Type:
Article