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Hereditary Sclerosing Poikiloderma
Journal of Korean Medical Science ; : 225-227, 2012.
Article in English | WPRIM | ID: wpr-33789
ABSTRACT
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
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Full text: Available Index: WPRIM (Western Pacific) Main subject: Rothmund-Thomson Syndrome / Sclerosis / Skin Diseases / Abnormalities, Multiple / Hyperpigmentation / Elastic Tissue / Fingers / Micrognathism Limits: Adolescent / Humans / Male Language: English Journal: Journal of Korean Medical Science Year: 2012 Type: Article

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Full text: Available Index: WPRIM (Western Pacific) Main subject: Rothmund-Thomson Syndrome / Sclerosis / Skin Diseases / Abnormalities, Multiple / Hyperpigmentation / Elastic Tissue / Fingers / Micrognathism Limits: Adolescent / Humans / Male Language: English Journal: Journal of Korean Medical Science Year: 2012 Type: Article