Clinical Features and Surgical Outcomes of Sturge-Weber Syndrome with Glaucoma
Journal of the Korean Ophthalmological Society
;
: 1737-1747, 2013.
Article
in Korean
| WPRIM
| ID: wpr-37755
ABSTRACT
PURPOSE:
To report clinical manifestations including neurocutaneous and ocular findings and to evaluate outcomes of trabeculectomy in patients with Sturge-Weber syndrome.METHODS:
The medical records of 10 eyes of 8 glaucoma patients with Sturge-Weber syndrome who were followed up for at least 1 year after trabeculectomy were reviewed retrospectively. We analyzed neurocutaneous and ocular findings, cumulative surgical success rates, and complications in patients with Sturge-Weber syndrome.RESULTS:
The mean patient age at the time of surgery was 12.6 +/- 13.0 years and mean follow-up period was 71.6 +/- 81.8 months. All patients showed various clinical findings including facial hemangioma (8 patients), seizure (6 patients), intracranial lesion (6 patients), developmental delay (4 patients), conjunctival/episcleral hemangioma (4 eyes), and choroidal hemangioma (4 eyes). Postoperative success was achieved in 8 out of 10 eyes (80.0%). Postoperatively, serous retinal detachment occurred in 2 out of 4 eyes with preoperative diffuse choroidal hemangioma.CONCLUSIONS:
Management of glaucoma associated with Sturge-Weber syndrome requires multidisciplinary treatment because of systemic involvement. Trabeculectomy appears to be an effective and relatively safe surgical option for glaucoma associated with Sturge-Weber syndrome. However, serious complications such as serous retinal detachment should be considered when planning trabeculectomy for patients with diffuse choroidal hemangioma.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Seizures
/
General Surgery
/
Retinal Detachment
/
Trabeculectomy
/
Sturge-Weber Syndrome
/
Glaucoma
/
Medical Records
/
Retrospective Studies
/
Follow-Up Studies
/
Choroid
Type of study:
Observational study
/
Prognostic study
Limits:
Humans
Language:
Korean
Journal:
Journal of the Korean Ophthalmological Society
Year:
2013
Type:
Article
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