Clinical Experiences of Uncommon Motor Neuron Disease: Hirayama Disease
Korean Journal of Spine
;
: 170-172, 2016.
Article
in English
| WPRIM
| ID: wpr-42835
ABSTRACT
Hirayama disease, juvenile muscular atrophy of the distal upper limb, is a rare disease predominantly affecting the anterior horn cells of the cervical spinal cord in young men. This cervical myelopathy is associated with neck flexion. It should be suspected in young male patients with a chronic history of weakness and atrophy involving the upper extremities followed by clinical stability in few years. Herein, we report 2 cases of Hirayama disease on emphasis of diagnostic approach and describe the pathognomonic findings at flexion magnetic resonance imaging.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Atrophy
/
Spinal Cord Diseases
/
Magnetic Resonance Imaging
/
Spinal Muscular Atrophies of Childhood
/
Motor Neuron Disease
/
Upper Extremity
/
Rare Diseases
/
Cervical Cord
/
Anterior Horn Cells
/
Motor Neurons
Limits:
Humans
/
Male
Language:
English
Journal:
Korean Journal of Spine
Year:
2016
Type:
Article
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