A Case of Kartagener's Syndrome with Various Ultrastructural Defects / 결핵
Tuberculosis and Respiratory Diseases
;
: 457-462, 2002.
Article
in Korean
| WPRIM
| ID: wpr-47446
ABSTRACT
Kartagener's syndrome is an inherited condition characterized by triad of chronic paranasal sinusitis, situs inversus, and bronchiectasis. Since 1976, Afzelius found a lack of dynein arm in immotile spermatozoa by electron microscopy, numerous recent studies have focused on the ultrastructural defect in the cilia and reported that the variety type of ultrastructural defect in immotile cilia syndrome. We report a female patient who had the Kartagener's triad with rare multiple ultrastructural defect of cilia in one patient. The electron microscopic examination showed partial dynein arm defect, loss of radial spoke, microtubular transposition, and giant cilia.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Arm
/
Sinusitis
/
Situs Inversus
/
Spermatozoa
/
Bronchiectasis
/
Microscopy, Electron
/
Kartagener Syndrome
/
Cilia
/
Ciliary Motility Disorders
/
Dyneins
Limits:
Female
/
Humans
Language:
Korean
Journal:
Tuberculosis and Respiratory Diseases
Year:
2002
Type:
Article
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