The first Korean case of poland-Mobius syndrome associated with dextrocardia / 소아과
Korean Journal of Pediatrics
;
: 1388-1391, 2009.
Article
in English
| WPRIM
| ID: wpr-55855
ABSTRACT
Poland syndrome is characterized by unilateral absence or hypoplasia of the pectoralis muscle and variable degree of ipsilateral hand anomalies. Mobius syndrome is a congenital neurological disorder characterized by complete or partial facial paralysis. Although the pathogeneses of these diseases are not well-characterized, diminished blood flow to the affected side is thought to play a role. A male infant weighing 2.670 g was born at 38+3 weeks of gestation with left facial paralysis, left chest wall defect with dextrocardia, and symbrachydactyly between the second and third fingers. The combination of Poland-Mobius syndrome is rare, and only 2 cases associated with dextrocardia have been reported worldwide. Here, we report the first case of Poland-Mobius syndrome associated with dextrocardia in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pectoralis Muscles
/
Poland Syndrome
/
Mobius Syndrome
/
Thoracic Wall
/
Dextrocardia
/
Facial Paralysis
/
Fingers
/
Hand
/
Korea
/
Nervous System Diseases
Limits:
Humans
/
Infant
/
Male
/
Pregnancy
Country/Region as subject:
Asia
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2009
Type:
Article
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