Congenital Hepatic Fibrosis: A case report
Korean Journal of Pathology
; : 50-53, 1991.
Article
in Ko
| WPRIM
| ID: wpr-58641
Responsible library:
WPRO
ABSTRACT
Congenital hepatic fibrosis is an uncommon disease of children and young adults with two major risks: gastrointestinal hemorrhage caused by portal hypertension, and cholangitis related to bacterial infection of dilated intrahepatic bile ducts. It is characterizeed by stony hard hepatomegaly and portal hypertension with rather well preserved hepatic function and architecture, and frequent association of the renal lesions. We have recently experienced a case of congenital hepatic fibrosis in a 24 year-old Korean male. The chief complaint was hematemesis from esophageal varices. There were marked hepatosplenomegaly, mild pancytopenia and the liver function test was within normal engorgement and dilatation of portal and splenic veins and multiple cysts of both kidneys.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Cysts
Limits:
Adult
/
Child
/
Female
/
Humans
/
Male
Language:
Ko
Journal:
Korean Journal of Pathology
Year:
1991
Type:
Article