Immunoglobulin G4 Related Retroperitoneal Fibrosis with Acute Kidney Injury: Report of A Case / 대한신장학회지

ABSTRACT

Immunoglobuin G4 (IgG4)-related sclerosing disease is a recently recognized syndrome characterized clinically by male predominance, elevated serum IgG4 level, and good response to steroid therapy. The pathologic characteristics are extensive lymphoplasmacytic infiltration with IgG4-positive cell and irregular fibrosis in various organs (pancreas, bile duct, salivary gland, retroperitoneum, kidney and lung). Some inflammatory pseudotumors may be involved in this disease. Herein, we experienced a case of IgG4-related retroperitoneal fibrosis with postrenal acute kidney injury and inflammatory pseudotumor of thyroid in a 31-year-old female who underwent insertion of double J catheter at both ureters and received corticosteroid treatment.