Xanthoma Disseminatum, a Case with Laryngeal Involvement / 대한이비인후과학회지
Korean Journal of Otolaryngology - Head and Neck Surgery
;
: 1065-1068, 2007.
Article
in Korean
| WPRIM
| ID: wpr-643964
ABSTRACT
Xanthoma disseminatum is a rare benign, normolipemic mucocutaneous xanthomatosis resulting due to the proliferation of non-Langerhans cell histiocytes. Xanthoma disseminatum typically involves the skin, particularly the flexor skin folds. Mucocutaneous involvement develops in 40-60% of patients, most commonly affecting the oropharynx, larynx, or corneae and conjunctivae. Xanthoma disseminatum may also manifest in the central nervous system. While the natural history of xanthoma disseminatum is usually benign, lesions in critical anatomical locations may result in morbidity and mortality. Curative therapy is lacking. We report a case with laryngeal involvement in a female patient. In this patient, xanthomas involved oropharynx and larynx mucosa. Dyspnea occurred due to epiglottis lesion. Tracheotomy was performed, and maintenance of breathing and decanulation were possible after epiglottectomy.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Oropharynx
/
Respiration
/
Skin
/
Tracheotomy
/
Xanthomatosis
/
Histiocytosis, Non-Langerhans-Cell
/
Central Nervous System
/
Mortality
/
Conjunctiva
/
Natural History
Type of study:
Prognostic study
Limits:
Female
/
Humans
Language:
Korean
Journal:
Korean Journal of Otolaryngology - Head and Neck Surgery
Year:
2007
Type:
Article
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