A Case of Malignant Peripheral Nerve Sheath Tumor of the Neck Associated with Neurofibromatosis Type I / 대한이비인후과학회지
Korean Journal of Otolaryngology - Head and Neck Surgery
;
: 657-660, 2010.
Article
in Korean
| WPRIM
| ID: wpr-654301
ABSTRACT
Neurofibromatosis is an autosomal dominant hereditary disorder characterized by skin abnormalities such as cafe au-lait spots, and soft tissue legion such as generalized subcutaneous neurofibroma. Malignant peripheral nerve sheath tumor is a spindle cell sarcoma that mostly arises in the soft tissue but rarely arises in the head and neck region. Malignant peripheral nerve sheath tumor can develop from the pre-existing neurofibromas or schwannomas, and from the peripheral nerves. They can also occur after radiation therapy. Malignant peripheral nerve sheath tumor is usually associated with neurofibromatosis type I. The authors recently experienced a case of malignant peripheral nerve sheath tumor associated with neurofibromatosis type I in a 20-year-old female patient who presented with a well marginated oval shape mass in the left neck.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Peripheral Nerves
/
Sarcoma
/
Skin Abnormalities
/
Neurofibromatosis 1
/
Neurofibromatoses
/
Nerve Sheath Neoplasms
/
Head
/
Neck
/
Neurilemmoma
/
Neurofibroma
Limits:
Female
/
Humans
Language:
Korean
Journal:
Korean Journal of Otolaryngology - Head and Neck Surgery
Year:
2010
Type:
Article
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