Peutz-Jeghers Syndrome with Recurrent Intussusception

ABSTRACT

The Peutz-Jeghers syndrome is an autosomal dominant hereditary disease characterized by hamartomatous polyps of the gastrointestinal tract and by mucocutaneous melanin deposits. This syndrome is clinically important because of the complication caused by the gastrointestinal polyp, leading to abdominal pain, gastrointestinal bleeding and intussusception. We experienced a case of Peutz-Jeghers syndrome associated with intussusception who was operated due to intussusception 14 years ago.