A Case of Neonatal Cholestasis Associated with Congenital Adrenal Hyperplasia / 대한소아소화기영양학회지
Korean Journal of Pediatric Gastroenterology and Nutrition
;
: 87-90, 2005.
Article
in Korean
| WPRIM
| ID: wpr-68796
ABSTRACT
It has been suggested that cortisol deficiency may be responsible for the cholestasis. Although congenital hypopituitarism was reported as a possible cause of neonatal cholestasis, congenital adrenal hyperplasia with neonatal cholestasis is a very rare report in the literature. We experienced a case presenting with neonatal cholestasis associated with congenital adrenal hyperplasia. This case provides a clinical evidence supporting the notion that cortisol has an important physiological role in bile acid synthesis and transport.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Bile
/
Hydrocortisone
/
Cholestasis
/
Adrenal Hyperplasia, Congenital
/
Hypopituitarism
Language:
Korean
Journal:
Korean Journal of Pediatric Gastroenterology and Nutrition
Year:
2005
Type:
Article
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