A Case of Congenital Hepatic Fibrosis Presented with Symptom of Acute Cholangitis / 대한소화기학회지
The Korean Journal of Gastroenterology
;
: 237-241, 2005.
Article
in Korean
| WPRIM
| ID: wpr-70842
ABSTRACT
Congenital hepatic fibrosis (CHF) is an autosomal recessive disease, presenting principally in children or young adults with portal hypertension, and infrequently associated with cholangitis. It is associated with renal malformation and Caroli's disease. The diagnosis of CHF is usually confirmed by its typical histological features. Cholangitis is a severe and frequently fatal complication. We report a 22-year-old man with congenital hepatic fibrosis who showed the cholangitis without radiological features of cystic dilatation or stone of intrahepatic ducts.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Cholangitis
/
Acute Disease
/
Liver Cirrhosis
Type of study:
Diagnostic study
Limits:
Adult
/
Humans
/
Male
Language:
Korean
Journal:
The Korean Journal of Gastroenterology
Year:
2005
Type:
Article
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