Management of Spontaneous Spinal Epidural Hematoma Developed in Children with Hemophilia / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
;
: 180-184, 2018.
Article
in Korean
| WPRIM
| ID: wpr-717636
ABSTRACT
Spinal epidural hematoma (SEH) is a rare neurosurgical emergency in which pressure on the spinal cord leads to acute neurological deficits, and is a rare complication in children with hemophilia. We report three cases of SEH in severe hemophilia A. An 8-month-old boy who presented with non-traumatic acute-onset irritability was found to have SEH and was later diagnosed with hemophilia. The two other patients presented with neck pain and magnetic resonance imaging confirmed the diagnosis of SEH. Two patients who received conservative management fully recovered, however the patient who presented with progressive neurological abnormalities at the time of diagnosis, received surgery but later developed breathing difficulties and quadriplegia. Early diagnosis and immediate, aggressive, clotting factor replacement therapy are crucial when managing SEH in children with hemophilia. Immediate and aggressive factor replacement, accompanied by both neurological monitoring and early imaging, are essential for hemophiliac with suspected SEH.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Quadriplegia
/
Respiration
/
Spinal Cord
/
Magnetic Resonance Imaging
/
Neck Pain
/
Early Diagnosis
/
Hematoma, Epidural, Spinal
/
Diagnosis
/
Emergencies
/
Hematoma
Type of study:
Diagnostic study
/
Screening study
Limits:
Child
/
Humans
/
Infant
/
Male
Language:
Korean
Journal:
Clinical Pediatric Hematology-Oncology
Year:
2018
Type:
Article
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