Surgical treatment of 22 patients with anomalous origin of one pulmonary artery branch / 中华实用儿科临床杂志

ABSTRACT

Objective To study the surgical treatment and outcome of anomalous origin of one pulmonary artery branch(AOPA).Methods Twenty-two patients (13 boys and 9 girls)with AOPA underwent surgical treatment,the age ranged from 1.5 months to 19.0 years old.Fifteen patients had anomalous origin of right pulmonary artery (AORPA),7 patients had anomalous origin of left pulmonary artery(AOLPA).The aorta-pulmonary window or interrupt aorta arch was found in the patients with AORPA,and the tetralogy of Fallot was only found in the patients with AOLPA.Eighteen procedures were performed by median sternotomy and cardiopulmonary bypass(CPB),4 cases were performed by off-CPB.The anomalous pulmonary artery was cut from the aorta at its origin and anastomosed to the lateral aspect of the main pulmonary artery,which sometimes artificial grafts or autologous pericardial were employed.Results One patient died during the operation because of crisis of pulmonary hypertense,and another patient died postoperatively of serious sepsis,the others were discharged healed.The mortality rate was 9％.The follow-up periods ranged from 6 to 149 months.All the patients were excellent but 1 patient was found a mild stenosis in the originate of right pulmonary artery.Conclusions It is important to correctly diagnosis and surgically treat for the patients with AOPA in time.A suitable surgical option by the pathological variation can obtain excellent result.