Moyamoya Syndrome: A Window of Moyamoya Disease
Journal of Korean Neurosurgical Society
;
: 408-414, 2015.
Article
in English
| WPRIM
| ID: wpr-73375
ABSTRACT
Moyamoya-like vasculopathy develops in association with various systemic diseases and conditions, which is termed moyamoya syndrome. Relatively common diseases and conditions are related to moyamoya syndrome, including neurofibromatosis type 1, Down syndrome, thyroid disease, and cranial irradiation. Moyamoya syndrome shares phenotypical characteristics with idiopathic moyamoya disease. However, they differ in other details, including clinical presentations, natural history, and treatment considerations. The study of moyamoya syndrome can provide clinicians and researchers with valuable knowledge and insight. Although it is infrequently encountered in clinical practice, moyamoya-like vasculopathy can severely complicate outcomes for patients with various underlying diseases when the clinician fails to expect or diagnose moyamoya syndrome development. Furthermore, moyamoya syndrome could be used as a doorway to more enigmatic moyamoya disease in research. More comprehensive survey and investigation are required to uncover the secrets of all the moyamoya-like phenomena.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Thyroid Diseases
/
Cranial Irradiation
/
Neurofibromatosis 1
/
Neurofibromatoses
/
Down Syndrome
/
Natural History
/
Moyamoya Disease
Limits:
Humans
Language:
English
Journal:
Journal of Korean Neurosurgical Society
Year:
2015
Type:
Article
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