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Herlyn-Werner-Wunderlich Syndrome: A Mini-review
Childhood Kidney Diseases ; : 12-16, 2018.
Article in English | WPRIM | ID: wpr-739188
ABSTRACT
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital malformation syndrome that is characterized by a triad of uterine didelphys, blind hemivagina, and ipsilateral renal agenesis. There is a wide variety of phenotypic presentation which is recognized as a spectrum of disease rather than a separate entity. The exact incidence and pathogenesis of HWW syndrome are yet to be investigated. While this disease typically involves adolescent girls who present with abdominal pain or a pelvic mass that is secondary to hematocolpos, nowadays, a majority of potential patients with HWW are being prenatally screened for renal anomalies. Therefore, it is recommended to search for uterovaginal anomalies whenever a multicystic dysplastic kidney or the absence of a kidney is noted in a newborn female, and the role of pediatric nephrologists has become ever more important for early recognition of the disease.
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Full text: Available Index: WPRIM (Western Pacific) Main subject: Abdominal Pain / Incidence / Multicystic Dysplastic Kidney / Hematocolpos / Kidney Type of study: Incidence study / Prognostic study Limits: Adolescent / Female / Humans / Infant, Newborn Language: English Journal: Childhood Kidney Diseases Year: 2018 Type: Article

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Full text: Available Index: WPRIM (Western Pacific) Main subject: Abdominal Pain / Incidence / Multicystic Dysplastic Kidney / Hematocolpos / Kidney Type of study: Incidence study / Prognostic study Limits: Adolescent / Female / Humans / Infant, Newborn Language: English Journal: Childhood Kidney Diseases Year: 2018 Type: Article