Chylous Manifestations and Management of Gorham-Stout Syndrome / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 44-46, 2019.
Article
in English
| WPRIM
| ID: wpr-742333
ABSTRACT
Gorham-Stout disease (GSD) was first described by Gorham and colleagues in 1954, but its precise mechanism and cause remain to be elucidated. In this condition, voluminous and potentially fatal chylous effusions into the thorax can occur. Herein, we describe a case of GSD in which the patient presented with massive pleural effusions and mottled osteolytic bone lesions. We performed multiple operations, including thoracic duct ligation using video-assisted thoracoscopic surgery and thoracotomic decortication, but these procedures did not succeed in preventing recurrent pleural effusion and chest wall lymphedema. After administering sirolimus (0.8 mg/m2, twice a day) and propranolol (40 mg, twice a day), the process of GSD in this patient has been controlled for more than 2 years.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pleural Effusion
/
Propranolol
/
Thoracic Duct
/
Thorax
/
Osteolysis, Essential
/
Chylothorax
/
Sirolimus
/
Thoracic Surgery, Video-Assisted
/
Thoracic Wall
/
Ligation
Limits:
Humans
Language:
English
Journal:
The Korean Journal of Thoracic and Cardiovascular Surgery
Year:
2019
Type:
Article
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