Severe Rhabdomyolysis in Phacomatosis Pigmentovascularis Type IIb associated with Sturge-Weber Syndrome / 대한구급학회지
The Korean Journal of Critical Care Medicine
;
: 329-335, 2015.
Article
in English
| WPRIM
| ID: wpr-770897
ABSTRACT
Phacomatosis pigmentovascularis (PPV) is a rare syndrome characterized by concurrent nevus flammeus (capillary malformation) and pigmentary nevus. According to current research, the major pathophysiologic mechanism in PPV is venous dysplasia with resultant compensatory collateral channels and venous hypertension. Arterial involvement is rare. We herein report our experience on renovascular hypertension, intermittent claudication, and severe rhabdomyolysis due to diffuse stenosis of multiple arteries in a patient with PPV type IIb associated with SWS.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Arteries
/
Rhabdomyolysis
/
Vascular Diseases
/
Sturge-Weber Syndrome
/
Intracranial Aneurysm
/
Constriction, Pathologic
/
Port-Wine Stain
/
Neurocutaneous Syndromes
/
Hypertension
/
Hypertension, Renovascular
Limits:
Humans
Language:
English
Journal:
The Korean Journal of Critical Care Medicine
Year:
2015
Type:
Article
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