Congenital Pulmonary Lymphangiectasia, Associated with Total Anomalous Pulmonary Venous Return
Korean Journal of Pathology
;
: 650-653, 2011.
Article
in English
| WPRIM
| ID: wpr-78177
ABSTRACT
Congenital pulmonary lymphangiectasia (CPL) is very rare. It shows diffuse pulmonary lymphatic dilatation without lymphatic proliferation. CPL can occur as a primary disorder or arise secondarily from other diseases such as the obstruction of pulmonary veins or lymphatics. The prognosis of CPL is very poor. Approximately 50% of infants are stillborn and most others usually die within the first day of life. The present case showed diffuse lymphangiectasia in the subpleural, interlobular, and peribronchovascular areas. The flat lining cells were immunohistochemically positive for D2-40 and CD31. CPL is usually diagnosed by clinicoradiological or postmortem examinations. However, our case was diagnosed by an antemortem lung biopsy. We report a case of CPL with total anomalous pulmonary venous return.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Prognosis
/
Pulmonary Veins
/
Scimitar Syndrome
/
Autopsy
/
Biopsy
/
Dilatation
/
Lung
Type of study:
Prognostic study
Limits:
Humans
/
Infant
Language:
English
Journal:
Korean Journal of Pathology
Year:
2011
Type:
Article
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