Case Report of Treatment of Multiple Odontogenic Keratocysts with Basal Cell Nevus Syndrome Using Preoperative Marsupialization andOrthodontic Extrusion
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
;
: 429-434, 2009.
Article
in Korean
| WPRIM
| ID: wpr-784915
ABSTRACT
Basal cell nevus syndrome is a rare inherited disorder characterized by mulitple cutaneous basal cell carcinoma, pits of the palms and soles, cysts of the jaws, skeletal abnormalities and ectopic calcifications. Currently there are new lines of investigation based on biomolecular studies, which aim at identifying the molecules responsible for these cysts and thus early allowing an early diagnosis of these patients. We report a case of a 9-year-old boy with the various manifestation of basal cell nevus syndrome, which are multiple odontogenic keratocysts, pits of the soles, bifid ribs, ectopic calcification, macrocephaly, and hypertelorism, etc. Total five odontogenic keratocysts were found. For the reduction of the size of the odontogenickeratocysts, following preoperative marsupialization, there were surgically enucleated. And the impacted upper right lateral incisor and canine are tracted orthodontically.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Ribs
/
Carcinoma, Basal Cell
/
Basal Cell Nevus Syndrome
/
Odontogenic Cysts
/
Early Diagnosis
/
Orthodontic Extrusion
/
Megalencephaly
/
Hypertelorism
/
Incisor
/
Jaw
Type of study:
Diagnostic study
/
Screening study
Limits:
Child
/
Humans
Language:
Korean
Journal:
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
Year:
2009
Type:
Article
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