A Malignant Solid Pseudopapillary Tumor of the Pancreas in a 14-year-old Girl / 임상소아혈액종양

ABSTRACT

Solid pseudopapillary tumor (SPT) is a rare, indolent pancreatic neoplasm of young women and the prognosis after surgical resection is quite favorable. However, several cases of forming metastasis, showing recurrence, or invading adjacent organs have been reported. We present a case of a 14-year-old girl with an infiltrating SPT who underwent distal pancreatectomy with splenectomy and adjuvant chemoradiotherapy. At surgery, the tumor was found to extend into the splenic hilum. On the basis of vascular invasion, capsular injury and pancreatic parenchymal infiltration, the diagnosis of malignant SPT of the pancreas was made. The patient received adjuvant chemoradiotherapy and she is alive without recurrence of disease for 26 months. Although most SPTs show relatively indolent behavior with low-grade malignancy, particular attention should be paid to the patients with pathology suggesting a possible malignant behavior.