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Successful Treatment of Erdheim-Chester Disease with Multisystemic Involvement in a 4-year-old Child by Interferon-α and Corticosteroid / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology ; : 69-74, 2017.
Article in English | WPRIM | ID: wpr-788593
ABSTRACT
Erdheim-Chester disease (ECD) is a rare form of proliferative non-Langerhans cell histiocytosis that involves multiple organs and is associated with a high mortality. The prognosis of ECD is variable, and it mainly depends on the involved anatomic sites. The treatment modalities have not been standardized, but interferon-α (IFN-α) has been reported to be effective in the management of ECD. ECD usually affects middle aged individuals with a slight male predominance but is extremely rare in children. We present an uncommon case of a 4-year-boy diagnosed with ECD who was treated with IFN-α and corticosteroid. He remained disease-free for 3 years after the completion of treatment.
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Full text: Available Index: WPRIM (Western Pacific) Main subject: Prognosis / Histiocytosis / Mortality / Erdheim-Chester Disease Type of study: Prognostic study Limits: Child / Child, preschool / Humans / Male Language: English Journal: Clinical Pediatric Hematology-Oncology Year: 2017 Type: Article

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Full text: Available Index: WPRIM (Western Pacific) Main subject: Prognosis / Histiocytosis / Mortality / Erdheim-Chester Disease Type of study: Prognostic study Limits: Child / Child, preschool / Humans / Male Language: English Journal: Clinical Pediatric Hematology-Oncology Year: 2017 Type: Article