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Recurrent Bilateral Branch Retinal Artery Occlusion with Hearing Loss and Encephalopathy: The First Case Report of Susac Syndrome in Korea
Journal of Korean Medical Science ; : 1518-1521, 2011.
Article in English | WPRIM | ID: wpr-82221
ABSTRACT
We report the first case of Susac syndrome in Koreans, in a 23-yr-old female patient who presented with sudden visual loss and associated neurological symptoms. Ophthalmic examination and fluorescein angiography showed multiple areas of branch retinal artery occlusion, which tended to recur in both eyes. Magnetic resonance imaging showed dot-like, diffusion-restricted lesions in the corpus callosum and left fornix, and audiometry showed low-frequency sensory hearing loss, compatible with Susac syndrome. She received immunosuppressive therapy with oral steroid and azathioprine. Three months later all the symptoms disappeared but obstructive vasculitis have been relapsing. This patient demonstrated the entire clinical triad of Susac syndrome, which tends to occur in young females. Although this disorder has rarely been reported in Asian populations, a high index of suspicion is warranted for early diagnosis and timely treatment.
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Full text: Available Index: WPRIM (Western Pacific) Main subject: Autoimmune Diseases / Azathioprine / Brain / Magnetic Resonance Imaging / Retinal Artery Occlusion / Susac Syndrome / Republic of Korea / Hearing Loss / Immunotherapy Type of study: Screening study Limits: Female / Humans Country/Region as subject: Asia Language: English Journal: Journal of Korean Medical Science Year: 2011 Type: Article

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Full text: Available Index: WPRIM (Western Pacific) Main subject: Autoimmune Diseases / Azathioprine / Brain / Magnetic Resonance Imaging / Retinal Artery Occlusion / Susac Syndrome / Republic of Korea / Hearing Loss / Immunotherapy Type of study: Screening study Limits: Female / Humans Country/Region as subject: Asia Language: English Journal: Journal of Korean Medical Science Year: 2011 Type: Article