Subacute sclerosing panencephalitis: Hyper acute variant

ABSTRACT

@#Subacute sclerosing panencephalitis (SSPE) usually presents insidiously. Acute presentations with a fulminant course can occur. However hyper acute presentations with a non-progressive course have not been reported. Here we describe two cases that had hyper acute presentation with occipital involvement misdiagnosed initially as ischemic infarct. One case remained stable for 4 years and then had a fulminant course and patient succumbed; the other patient continued to remain stable at 2 year follow up. In countries where SSPE is prevalent, it is important to be aware of such a variant of SSPE.