Cerebellar Hemangioblastoma Associated with Polycythemia: Case Report

ABSTRACT

We have experienced a case of cerebellar hemangioblastoma associated with polycythemia in 44-year old male adult who has suffered from the headache, chocked disc and visual disturbance for about 1 year and 4 months. A marked polycythemia was found but retinal angioma, cysts on the pancreas and kidney and then familial incidence were not detected. The signs of increased intracranial pressure was marked, accompanying the decreased visual acuity. Liver and spleen were not palpable. On bilateral carotid angiogram, it revealed a severe hydrocephalus, on Conray ventriculogram, obstruction of 4th ventricle by huge mass in the posterior fossa. The right vertebral angiography revealed a midline hen egg sized tumor mass which was highly vascular and was supplied mainly by PICA, SCA and PCA brances. Brain C-T scan showed the vascular mass in midline of posterior fossa by enhancement. We operated the cerebellar tumor which was solid. The uncontrollable bleeding was encountered. We performed the biopsy which revealed a hemangioblastoma. Inspite of the V-A shunt, the patient expired suddenly on 5th post-operative day.