Extensive and aggressive growth of adenoid cysticcarcinoma in the lacrimal gland

ABSTRACT

Adenoid cystic carcinoma (ACC) in the lacrimal gland is a very rare disease with poor overall prognosis.Its primary treatment is surgical excision, including orbital exenteration and radical orbitectomy,which is combined with radiotherapy and chemotherapy. Age, histopathologic type, boneinvasion, and tumor extent are known factors that affect the prognosis of ACC. Furthermore, perineuralinvasion is highly associated with local tumor recurrence and tumor base invasion. Here,we report a rare case of ACC in the lacrimal gland with superior sagittal sinus invasion that repeatedlyrecurred after the surgical excision.