Three Cases of Outer Retinal Tubulation in Bietti's Crystalline Dystrophy
Journal of the Korean Ophthalmological Society
;
: 1141-1148, 2015.
Article
in Korean
| WPRIM
| ID: wpr-83162
ABSTRACT
PURPOSE:
To report the prevalence and the characteristics of outer retinal tubulation (ORT) in Bietti's crystalline dystrophy in 6 eyes of 3 patients. CASESUMMARY:
Three patients with Bietti's crystalline dystrophy were examined using color fundus photography, fundus autofluorescence picture, spectral domain optical coherence tomography (SD-OCT), fluorescein angiography, electroretinogram and electrooculogram. ORT was detected in 3 of 3 (100%) Bietti's crystalline dystrophy patients. SD-OCT B-scan revealed hyperreflective material inside the hyporeflective internal space with hyperreflective border. ORT was observed under the fovea or outside the fovea and on the outer nuclear layer in the retina. ORTs were no greater than 70 x 140 microm in size when measured using SD-OCT B-scan image.CONCLUSIONS:
ORT was observed frequently in patients with Bietti's crystalline dystrophy. These findings can potentially predict the extensive photoreceptor abnormalities in retinal pigment epithelial atrophy.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Retina
/
Retinaldehyde
/
Atrophy
/
Fluorescein Angiography
/
Photography
/
Prevalence
/
Crystallins
/
Tomography, Optical Coherence
/
Electrooculography
Type of study:
Prevalence study
/
Prognostic study
Limits:
Humans
Language:
Korean
Journal:
Journal of the Korean Ophthalmological Society
Year:
2015
Type:
Article
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