Subcutaneous Panniculitis-Like T-Cell Lymphoma with Hemophagocytic Syndrome in a Child: A Successful Treatment with the BFM-NHL-90 Protocol / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
;
: 129-133, 2020.
Article
| WPRIM
| ID: wpr-832102
ABSTRACT
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a distinct cutaneous lymphoma subtype that is characterized by pleomorphic T-cell infiltration of the subcutaneous tissue. SPTCL is usually associated with indolent clinical course. However, it can be complicated by hemophagocytic syndrome (HPS), which leads to worse prognosis. Childhood SPTCL is rare and there is no standardized treatment regimen of SPTCL with HPS. Here we report a pediatric case of SPTCL with HPS who responded favorably with multi-agent chemotherapy of the BFM (Berlin‐Frankfurt‐Münster)-NHL (non-Hodgkin lymphoma)-90 protocol.
Full text:
Available
Index:
WPRIM (Western Pacific)
Type of study:
Practice guideline
Journal:
Clinical Pediatric Hematology-Oncology
Year:
2020
Type:
Article
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