MRI Findings of Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA syndrome) with a Blind Megaureter: Case Report
Investigative Magnetic Resonance Imaging
;
: 196-199, 2015.
Article
in English
| WPRIM
| ID: wpr-90698
ABSTRACT
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is an uncommon congenital abnormality of the female urogenital tract characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magnetic resonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructed hemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, a well-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seen in the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginal septotomy and drainage of hematometrocolpos were done initially, but unilateral hysterectomy was later performed to relieve the patient's symptoms. The cystic mass in the right lower pelvic cavity was also excised and confirmed as a blind megaureter.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Congenital Abnormalities
/
Urinary Bladder
/
Magnetic Resonance Imaging
/
Abdominal Pain
/
Drainage
/
Hysterectomy
Type of study:
Diagnostic study
Limits:
Adolescent
/
Female
/
Humans
Language:
English
Journal:
Investigative Magnetic Resonance Imaging
Year:
2015
Type:
Article
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