A Case of Multifocal Fibrosclerosis with CNS Involvement
Journal of the Korean Neurological Association
;
: 372-377, 1990.
Article
in Korean
| WPRIM
| ID: wpr-91170
ABSTRACT
Multifocal fibrosclerosis, a rare disorder, has no known etiology and is considered to be a systemic illness manifested by combinations of fibrosing process of multiple areas such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing cholangitis, and Reidel's thyroiditis. We have experienced a 49-year-old man with pseudotumor of the orbit, sclerosing cholangitis, and CNS involvements included unrecognized meningitis and suspicious CNS vasculitis. The patient showed clinical improvement with corticosteroid therapy.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Orbit
/
Retroperitoneal Fibrosis
/
Thyroid Gland
/
Thyroiditis
/
Fibrosis
/
Cholangitis, Sclerosing
/
Orbital Pseudotumor
/
Vasculitis, Central Nervous System
/
Meningitis
Limits:
Humans
Language:
Korean
Journal:
Journal of the Korean Neurological Association
Year:
1990
Type:
Article
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