Absence of the Intrahepatic Inferior Vena Cava with Polysplenia Syndrome on Multidetector Computed Tomography: A Case Report

ABSTRACT

Various anomalies of the inferior vena cava (IVC) can arise from a failure in the normal embryogenic processes. Agenesis of the intrahepatic segment of the IVC with azygos continuation, which is caused by failure of formation of the right subcardinal–hepatic anastomosis, is a rare IVC anomaly. In this paper, we report a case of interrupted IVC with azygos vein continuation, combined with polysplenia, intestinal malrotation, and truncated pancreas, which was incidentally found on abdominal CT and thoracic aorta CT angiography.