A Case of POEMS Syndrome Previously Diagnosed with Extramedullary Plasmacytoma / 대한신경근육질환학회지
Korean Journal of Neuromuscular Disorders
;
(2): 59-63, 2021.
Article
in Korean
| WPRIM
| ID: wpr-917946
ABSTRACT
POEMS (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes) syndrome is a rare multisystem disorder associated with osteosclerotic myeloma. It is characterized by peripheral polyneuropathy, presence of monoclonal plasma cell proliferative disorder, and one or more of the following features – sclerotic bone lesions, Castleman disease, elevated levels of vascular endothelial growth factor, organomegaly, extravascular volume overload, endocrinopathy, skin changes, papilledema, and thrombocytosis. Extramedullary plasmacytoma (EMP) is a rare plasma cell neoplasm that arises in isolated tissues without bone marrow involvement or systemic characteristics of multiple myeloma. Herein, we report a male patient who was previously diagnosed with EMP and later developed POEMS.
Full text:
Available
Index:
WPRIM (Western Pacific)
Type of study:
Diagnostic study
Language:
Korean
Journal:
Korean Journal of Neuromuscular Disorders
Year:
2021
Type:
Article
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