Hirayama Disease with Proximal Involvement
Journal of Korean Medical Science
; : 1664-1667, 2016.
Article
in En
| WPRIM
| ID: wpr-93744
Responsible library:
WPRO
ABSTRACT
Hirayama disease is a slowly progressing benign motor neuron disease that affects the distal upper limb. A 29-year-old man visited the hospital with a 1-year history of weakened left proximal upper limb. He was diagnosed with Hirayama disease 9 years ago, while there was no further progression of the muscle weakness afterward. Atrophy and weakness was detected in proximal upper limb muscles. Magnetic resonance imaging and somatosensory evoked potentials were normal. Needle electromyography showed abnormal findings in proximal upper limb muscles. Our patient had Hirayama disease involving the proximal portion through secondary progression. Clinical manifestation and accurate electromyography may be useful for diagnosis. Rare cases with progression patterns as described here are helpful and have clinical meaning for clinicians.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Atrophy
/
Magnetic Resonance Imaging
/
Motor Neuron Disease
/
Muscle Weakness
/
Upper Extremity
/
Diagnosis
/
Electromyography
/
Evoked Potentials, Somatosensory
/
Muscles
/
Needles
Type of study:
Diagnostic_studies
Limits:
Adult
/
Humans
Language:
En
Journal:
Journal of Korean Medical Science
Year:
2016
Type:
Article