A Case of Pseudoxanthoma Elasticum Clinically Mimicking Cutis Laxa / 대한피부과학회지
Korean Journal of Dermatology
;
: 227-230, 2000.
Article
in Korean
| WPRIM
| ID: wpr-95554
ABSTRACT
Pseudoxanthoma elasticum is a rare, heritable, systemic disease of connective tissue characterized by degeneration of elastic fiber and mainly affects the skin, eye and blood vessels. We report a case of pseudoxanthoma elasticum mimicking cutis laxa. She had a generalized laxity of the skin for about 30 years. There were similar skin lesions in her sister. No other systemic involvement was found. Histopathologic examination revealed clumping, fragmentation and calcification of elastic fibers in the dermis.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pseudoxanthoma Elasticum
/
Skin
/
Blood Vessels
/
Connective Tissue
/
Dermis
/
Cutis Laxa
/
Siblings
/
Elastic Tissue
Limits:
Humans
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2000
Type:
Article
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