A Case of Adult Polyglucosan Body Disease
Yonsei Medical Journal
;
: 701-703, 2007.
Article
in English
| WPRIM
| ID: wpr-96524
ABSTRACT
Adult polyglucosan body disease (APBD) is a rare neurological disease, characterized by adult onset (fifth to seventh decades), progressive sensorimotor or pure motor peripheral neuropathy, upper motor neuron symptoms, neurogenic bladder, and cognitive impairment. APBD is confirmed by a sural nerve biopsy that shows the widespread presence of polyglucosan bodies in the nerve. We report a 70 year old male patient who exhibited progressive weakness in all extremities and dementia. His electrodiagnostic studies showed sensorimotor polyneuropathy and muscle pathology that consisted of polyglucosan bodies located in small peripheral nerves. This is the first case of APBD reported in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Biopsy
/
Inclusion Bodies
/
Neurodegenerative Diseases
/
Glucans
Limits:
Aged
/
Humans
/
Male
Language:
English
Journal:
Yonsei Medical Journal
Year:
2007
Type:
Article
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