Pulmonary alveolar proteinosis in a 15-year-old girl
Allergy, Asthma & Respiratory Disease
;
: 86-89, 2015.
Article
in Korean
| WPRIM
| ID: wpr-99816
ABSTRACT
Pulmonary alveolar proteinosis (PAP) is a diffuse lung disease characterized by the accumulation of lipoproteins derived from surfactants in the distal air space. The lack of granulocyte macrophage colony-stimulating factor is believed to contribute to macrophage dysfunction and the impaired processing of surfactants. Because the prevalence of PAP in the general population is less than 1 in 200,000, and the typical age at presentation is 35 to 50 years, PAP is a very rare disease in children. To the best of our knowledge, there has been no Korean report on PAP in children. We describe here a patient who was diagnosed with PAP at the aged 15 years.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pulmonary Alveolar Proteinosis
/
Surface-Active Agents
/
Prevalence
/
Macrophage Colony-Stimulating Factor
/
Rare Diseases
/
Granulocytes
/
Lipoproteins
/
Lung Diseases
/
Macrophages
Type of study:
Prevalence study
Limits:
Adolescent
/
Child
/
Female
/
Humans
Language:
Korean
Journal:
Allergy, Asthma & Respiratory Disease
Year:
2015
Type:
Article
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