Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report
São Paulo med. j
;
137(2): 206-208, Mar.-Apr. 2019. tab, graf
Artículo
en Inglés
| LILACS
| ID: biblio-1014634
ABSTRACT
ABSTRACT CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient's clinical characteristics. CASE REPORT: A 42-year-old female patient was operated to treat a retroperitoneal mass. The diagnosis was established as PEComa with benign behavior. Two years after the diagnosis, chest and abdominal computed tomography scans showed intra-abdominal recurrence and lymphangioleiomyomatosis in the lung. Treatment with everolimus was started. The disease stabilized in the third month of treatment, according to the response evaluation criteria in solid tumors. CONCLUSION: PEComas are tumors with unpredictable behavior. Therefore, these patients require long-term follow-up, even in cases of correct diagnosis and benign PEComa.
Texto completo:
Disponible
Índice:
LILACS (Américas)
Asunto principal:
Neoplasias Retroperitoneales
/
Linfangioleiomiomatosis
/
Neoplasias de Células Epitelioides Perivasculares
Tipo de estudio:
Estudio diagnóstico
Límite:
Adulto
/
Femenino
/
Humanos
Idioma:
Inglés
Revista:
São Paulo med. j
Asunto de la revista:
Cirurgia Geral
/
Cincia
/
Ginecologia
/
Medicina
/
Medicina Interna
/
Obstetr¡cia
/
Pediatria
/
Sa£de Mental
/
Sa£de P£blica
Año:
2019
Tipo del documento:
Artículo
País de afiliación:
Turquía
Institución/País de afiliación:
Kayseri Egitimve Arastirma Hastanesi/TR
Similares
MEDLINE
...
LILACS
LIS