Update on Coronary Involvement in Fabry Disease
J. inborn errors metab. screen
;
4: e160005, 2016. graf
Artículo
en Inglés
|
LILACS-Express
| LILACS
| ID: biblio-1090903
ABSTRACT
Abstract Fabry disease is a multisystemic disorder with consequent morbidity and mortality at an early age in patients of both genders. Although renal failure has been previously described as the cause of death with the highest prevalence, recent studies, based on the analysis of the population recorded in the Fabry Registry, reported that 40% of deaths had a cardiovascular origin. Data from the same registry emphasize the high risk for these patients suffering cardiovascular events—particularly acute myocardial infarction—and to the fact that this risk is higher for those patients who need dialysis. Microvascular dysfunction is a constant in patients with Fabry disease, which affects young patients, independently from other cardiac involvement manifestations—such as left ventricular hypertrophy—and from the patient's gender.
Texto completo:
Disponible
Índice:
LILACS (Américas)
Tipo de estudio:
Factores de riesgo
Idioma:
Inglés
Revista:
J. inborn errors metab. screen
Asunto de la revista:
Medicina Cl¡nica
/
Patologia
Año:
2016
Tipo del documento:
Artículo
País de afiliación:
Argentina
Institución/País de afiliación:
Centro Cardiovascular Bolivar/AR
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