Pseudosarcoma in marfan's syndrome : a case study

ABSTRACT

Pseudosarcomatous fasciitis was reported by Knowaler et al in 1955. It is a benign and quasi-neoplastic proliferation of fibroblasts; which is often mistaken for a sarcoma because of its rapid growth; rich cellularity and mitotic activity. It is one of the more common soft tissue lesions and exceeds in frequency other tumor or tumor-like lesions of fibrous tissue. This attested to by the more than 1000 cases that were reviewed at the American Armed Forces Institute of Pathology (AFIP) in a 20 year period. The case of pseudosarcoma occuring in a patient with marfan's syndrome in Seychelles is reported