Cardiac involvement in Erdheim-Chester disease: a case report
Clin. biomed. res
;
34(4): 406-409, 2014. ilus
Artículo
en Inglés
| LILACS
| ID: biblio-834475
ABSTRACT
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.
Texto completo:
Disponible
Índice:
LILACS (Américas)
Asunto principal:
Ecocardiografía
/
Enfermedad de Erdheim-Chester
/
Insuficiencia Cardíaca
Límite:
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Clin. biomed. res
Asunto de la revista:
Medicina
Año:
2014
Tipo del documento:
Artículo
País de afiliación:
Brasil
Institución/País de afiliación:
Hospital de Clínicas de Porto Alegre/BR
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