Association of amyloidosis cutis dyschromica and familial Mediterranean fever
An. bras. dermatol
;
92(5,supl.1): 21-23, 2017. graf
Artículo
en Inglés
| LILACS
| ID: biblio-887101
ABSTRACT
Abstract: Amyloidosis cutis dyschromica is a rare type of primary cutaneous amyloidosis characterized by reticulate hyper-pigmentation with discrete hypopigmented macules. Up to date, about 50 cases of amyloidosis cutis dyschromica have been reported and the majority are familial cases of Asian ethnicity. Various diseases, particularly autoimmune diseases such as systemic sclerosis and systemic lupus erythematosus, have been associated with amyloidosis cutis dyschromica. Herein, we report a case of amyloidosis cutis dyschromica accompanying familial Mediterranean fever with a delayed diagnosis of 40 years. To the best of our knowledge, this is the first report of the association of amyloidosis cutis dyschromica and familial mediterranean fever.
Texto completo:
Disponible
Índice:
LILACS (Américas)
Asunto principal:
Fiebre Mediterránea Familiar
/
Enfermedades Cutáneas Genéticas
/
Amiloidosis Familiar
Tipo de estudio:
Factores de riesgo
Límite:
Femenino
/
Humanos
Idioma:
Inglés
Revista:
An. bras. dermatol
Asunto de la revista:
Dermatologia
Año:
2017
Tipo del documento:
Artículo
País de afiliación:
Turquía
Institución/País de afiliación:
Mugla Sitki Kocman University Training and Research Hospital/TR
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