Celiac Crisis: an unusual presentation of gluten-sensitive enteropathy
Autops. Case Rep
; 8(3): e2018027, July-Sept. 2018. ilus, tab
Article
en En
| LILACS
| ID: biblio-911941
Biblioteca responsable:
BR26.7
ABSTRACT
Celiac disease (CD)also known as gluten-sensitive enteropathyis a chronic, genetically predisposing and autoimmune entity with a wide range of clinical manifestations triggered by gluten ingestion, which affects 1% of the general population. Currently, up to 60% of the diagnosis of CD is in adults due to the atypical course of the disease. The severe acute onset of CDalso called celiac crisisis very uncommon and is still not well documented in adults. We report the case of a 58-year-old man who presented a 45-day history of subtle-onset diarrhea followed by malabsorption syndrome with progressive weight loss, anasarca, and electrolyte disturbances. The diagnostic work-up included an upper digestive endoscopy, which showed scalloping of the duodenal mucosa with pathological features confirmed on biopsies. Specific antibodies were positive, and a satisfactory clinical response was obtained once a gluten-free diet was started. Celiac crisis is a rare initial presentation of CD characterized by severe diarrhea, dehydration, weight loss, hypoproteinemia, and metabolic and electrolyte disturbances. Although rare, it should be considered in patients with apparently unexplained chronic diarrhea.
Palabras clave
Texto completo:
1
Índice:
LILACS
Asunto principal:
Enfermedad Celíaca
/
Diarrea
/
Síndromes de Malabsorción
Tipo de estudio:
Diagnostic_studies
Límite:
Humans
/
Male
Idioma:
En
Revista:
Autops. Case Rep
Asunto de la revista:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Año:
2018
Tipo del documento:
Article